Intravenous anesthesia


Anesthesia and Pain Medicine. 2005 Dec. 9(4): 215-219
ⓒ Korean Society for Intravenous Anesthesia
Anesthetic Management of Osteogenesis Imperfecta -Two cases reports-
Won Ho Kim, M.D., Hyun Joo Ahn, M.D., and Mi Sook Gwak, M.D.
Department of Anesthesiology and Pain Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea

Osteogenesis imperfecta is a rare genetic disorder of connective tissues. It is featured like fragile bone, the risk of malignant hyperthermia, congenital heart disease, severe restrictive lung disease, cor pulmonale, and bleeding tendency. There are several points to empathize for anesthesia of osteogenesis imperfecta. Those are a preoperative cardiopulmonary screening, an appropriate anesthesia, a careful monitoring for malignant hyperthermia and a gentle handling of the patient to avoid fracture. Two patients of osteogenesis imperfecta who are a sister and a brother undergone anesthesias and operations successfully and discharged from our hospital without complications. The sister who received scoliosis operation was anesthetized with isoflurane, and the brother who undergone osteotomy and intramedullary nailing of both legs with total intravenous technique. Through the anesthesias, they did not show malignant hyperthermia related symptoms and other unpredictable events.
Key words : complications, intravenous anesthesia, osteogenesis imperfecta, volatile anesthetics.
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